AAV-mediated intramuscular delivery of myotubularin corrects the myotubular myopathy phenotype in targeted murine muscle and suggests a function in plasma membrane homeostasis

Anna Buj‐Bello(Pediatrics and Genetics), Jean‐Louis Mandel(Centre National de la Recherche Scientifique), Alan H. Beggs(Boston Children's Hospital), Patrice Denèfle(Sofia University), Muriel Durand(Genethon (France)), Yannick Schwab(European Molecular Biology Laboratory), Nadia Messaddeq(Inserm), Patrick Schultz(Centre National de la Recherche Scientifique), Olivier Danos(Regenxbio (United States)), Anne‐Marie Douar(Genethon (France)), Françoise Fougerousse(Genethon (France)), Marie Montus(Genethon (France)), Danièle Spehner(Inserm), Christopher R. Pierson(Nationwide Children's Hospital), Christine Kretz(Pediatrics and Genetics)
Human Molecular Genetics
April 22, 2008
Cited by 127


Related Papers