Antisense Proline-Arginine RAN Dipeptides Linked to C9ORF72-ALS/FTD Form Toxic Nuclear Aggregates that Initiate In Vitro and In Vivo Neuronal Death

Xinmei Wen(Thomas Jefferson University), Davide Trotti(Thomas Jefferson University), Wenzhi Tan(Chonnam National University), Thomas Westergard(Thomas Jefferson University), Justin K. Ichida(University of Southern California), Karthik Krishnamurthy(Thomas Jefferson University), Udai Bhan Pandey(University of Pittsburgh), Neil A. Shneider(Columbia University Irving Medical Center), Yingxiao Shi(University of Southern California), Shashirekha S. Markandaiah(Thomas Jefferson University), Shao‐Yu Lin(University of Southern California), John Monaghan(Children's Hospital of Pittsburgh), Piera Pasinelli(Thomas Jefferson University)
Neuron
December 1, 2014
10.1016/j.neuron.2014.12.010
Cited by 556

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