Endosomal Accumulation of Toll-Like Receptor 4 Causes Constitutive Secretion of Cytokines and Activation of Signal Transducers and Activators of Transcription in Niemann–Pick Disease Type C (NPC) Fibroblasts: A Potential Basis for Glial Cell Activation in the NPC Brain
Michitaka Suzuki(Nagoya University), Haruaki Ninomiya(Tottori University), Joanna P. Davies(Icahn School of Medicine at Mount Sinai), Makoto Ueno(Child Neurology Associates), Kousaku Ohno(Sanin Rosai Hospital), Yuko Sugimoto(Tottori University), Yukisato Kitamura(Tottori University), Hiroshi Hosokawa(Kyoto University), Marie T. Vanier(Inserm), Yiannis A. Ioannou(Icahn School of Medicine at Mount Sinai), Yuki Ohsaki(Tottori University), Shinsuke Kato(The University of Tokyo)
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