Medium‐chain triglycerides supplement therapy with a low‐carbohydrate formula can supply energy and enhance ammonia detoxification in the hepatocytes of patients with adult–onset type II citrullinemia
Kiyoshi Hayasaka(Yamagata University), Hiroshi Yoshida(Tokyo National Hospital), Hiroshi Mitsubuchi(Kumamoto University Hospital), Mitsunori Yamakawa(Yamagata University), Tetsuo Mitsui(Yamagata University), Takahiro Nakayama(University of Shizuoka), Hiromasa Ohira(Fukushima Medical University), Yasuo OCHIAI(Saiseikai Utsunomiya hospital), Noriyo Yamashiki(The University of Tokyo), Hisayoshi Watanabe(Iwate Medical University), Masahide Yazaki, Takashi Kon(Yamagata City Hospital Saiseikan), Toshiyuki Tahara(Saiseikai Utsunomiya hospital), Hiroaki Haga(Yamagata University), Tamio Nakahara(Shiga University of Medical Science), Chikahiko Numakura(Yamagata University)
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