ELEVATED PHENYLACETIC ACID LEVELS DO NOT CORRELATE WITH ADVERSE EVENTS IN PATIENTS WITH UREA CYCLE DISORDERS OR HEPATIC ENCEPHALOPATHY AND CAN BE PREDICTED BASED ON THE PLASMA PAA TO PAGN RATIO

Masoud Mokhtarani, Bruce F. Scharschmidt, Cary O. Harding(Oregon Health & Science University), Andreas Schulze(University of Toronto), Parvez Mantry(Methodist Dallas Medical Center), Klara Dickinson, Marwan Ghabril, Douglas Milikien, John M. Vierling(Baylor College of Medicine), George A. Díaz(Icahn School of Medicine at Mount Sinai), Dion F. Coakley, William Berquist(Palo Alto University), Wally R. Smith(Virginia Commonwealth University), Catherine J. Norris, Don C. Rockey(Medical University of South Carolina), Cynthia LeMons(National Urea Cycle Disorders Foundation), B. Lee(Baylor College of Medicine), Tristen Moors, Uta Lichter‐Konecki(Children's National), Nicola Longo(Center for Human Genetics), Annette Feigenbaum(Hospital for Sick Children), Shawn E. McCandless(University Hospitals of Cleveland), James Bartley(MemorialCare Long Beach Medical Center), S.C. Nagamani(Baylor College of Medicine), Renata C. Gallagher(Children's Hospital Colorado), Susan A. Berry(University of Minnesota), Robert S. Brown(Washington University Medical Center), William J. Rhead(Children's Hospital of Wisconsin)
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December 1, 2013
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