Cystic fibrosis lung disease starts in the small airways: Can we treat it more effectively?

Harm A.W.M. Tiddens(Erasmus MC), Peter D. Paré(University of British Columbia), Scott H. Donaldson(University of North Carolina at Chapel Hill), Margaret Rosenfeld(Seattle Children's Hospital)

Pediatric Pulmonology

January 15, 2010

10.1002/ppul.21154

Cited by 180

Related Papers

Effect of VX-770 in Persons with Cystic Fibrosis and the G551D- <i>CFTR</i> Mutation

|New England Journal of Medicine|2010|802

Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the <i>F508del-CFTR</i> mutation

|Thorax|2011|496

Multiple-breath inert gas washout and spirometry versus structural lung disease in cystic fibrosis

|Thorax|2007|364

Decline in NRF2-regulated Antioxidants in Chronic Obstructive Pulmonary Disease Lungs Due to Loss of Its Positive Regulator, DJ-1

|American Journal of Respiratory and Critical Care Medicine|2008|354

Tracheomalacia and Bronchomalacia in Children

|CHEST Journal|2005|326