Mitochondrial succinate is instrumental for HIF1α nuclear translocation in SDHA-mutant fibroblasts under normoxic conditions

Jean-Jacques Brière, Pierre Rustin(Inserm), Judith Favier(Inserm), Vincent El Ghouzzi(Inserm), Paule Bénit(Inserm), Maria Flavia Di Renzo(Cancer Genetics (United States)), Annalisa Lorenzato(University of Turin), Daniel Rabier(Hôpital Necker-Enfants Malades), Anne‐Paule Gimenez‐Roqueplo(Délégation Paris 5)
Human Molecular Genetics
September 29, 2005
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