Characteristic Multiorgan Pathology of Cystic Fibrosis in a Long-Living Cystic Fibrosis Transmembrane Regulator Knockout Murine Model

Peter R. Durie(University of Toronto), Cameron Ackerley(University of Toronto), M. J. Phillips(University of Toronto), Geraldine Kent(Hospital for Sick Children)

American Journal Of Pathology

April 1, 2004

10.1016/s0002-9440(10)63234-8

Cited by 158

Related Papers

Effect of VX-770 in Persons with Cystic Fibrosis and the G551D- <i>CFTR</i> Mutation

|New England Journal of Medicine|2010|802

Recruitment of functional GABAA receptors to postsynaptic domains by insulin

|Nature|1997|536

Definitions of Pediatric Pancreatitis and Survey of Present Clinical Practices

|Journal of Pediatric Gastroenterology and Nutrition|2012|508

Results of a phase IIa study of VX-809, an investigational CFTR corrector compound, in subjects with cystic fibrosis homozygous for the <i>F508del-CFTR</i> mutation

|Thorax|2011|501

Expression of the cystic fibrosis gene in non-epithelial invertebrate cells produces a regulated anion conductance

|Cell|1991|500