Defective CFTR induces aggresome formation and lung inflammation in cystic fibrosis through ROS-mediated autophagy inhibition

Alessandro Luciani(Cystic Fibrosis Research Foundation), Valeria Rachela Villella(Federico II University Hospital), Speranza Esposito(University of Foggia), Nicola Brunetti‐Pierri(Federico II University Hospital), Diego L. Medina(Telethon Institute Of Genetics And Medicine), Carmine Settembre(Telethon Institute Of Genetics And Medicine), Manuela Gavina(Vita-Salute San Raffaele University), Laura Pulze(San Raffaele University of Rome), Ida Giardino(University of Foggia), Massimo Pettoello‐Mantovani(University of Foggia), Maria D’Apolito(University of Foggia), Stefano Guido(Federico II University Hospital), Eliezer Masliah(University of California, San Diego), Brian Spencer(University of California, San Diego), Sonia Quaratino, Valeria Raia(Federico II University Hospital), Andrea Ballabio(Telethon Institute Of Genetics And Medicine), Luigi Maiuri(University of Foggia)
Nature Cell Biology
August 15, 2010
Cited by 460

Abstract


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