Polyglutamine- and Temperature-Dependent Conformational Rigidity in Mutant Huntingtin Revealed by Immunoassays and Circular Dichroism Spectroscopy
Valentina Fodale(IRBM Science Park), Andrea Caricasole(Kedrion (Italy)), Robert E. Pacifici(CHDI Foundation), Douglas Macdonald(TAE Technologies, Inc (United States)), Lucia Azzollini(Axxam (Italy)), Hyunsun Park, J. Mario Isas(Keck Hospital of USC), Andreas Weiss(Novartis (China)), Roberto Boggio(IRBM Science Park), Margherita Verani(Illinois Railway Museum), Ryan C. Schoenfeld(CHDI Foundation), Cristina Cariulo(Illinois Railway Museum), Natalie C. Kegulian(University of Southern California), Alessandro Padova(IRBM Science Park), Lara Petricca(IRBM Science Park), Ralf Langen(Keck Hospital of USC), Rainer Kühn(IRBM Science Park), Manuel Daldin(IRBM Science Park)
Cited by 48
Related Papers
Protein misfolding in neurodegenerative diseases: implications and strategies
|Translational Neurodegeneration|2017|671
Mutation of SHOC2 promotes aberrant protein N-myristoylation and causes Noonan-like syndrome with loose anagen hair
|Nature Genetics|2009|417
Induction of Dickkopf-1, a Negative Modulator of the Wnt Pathway, Is Associated with Neuronal Degeneration in Alzheimer's Brain
|Journal of Neuroscience|2004|394
Membrane Curvature Induction and Tubulation Are Common Features of Synucleins and Apolipoproteins
|Journal of Biological Chemistry|2010|318