Extracellular magnesium and calcium reduce myotonia in isolated ClC‐1 chloride channel‐inhibited human muscle
Martin Skov(Aarhus University), Thomas Holm Pedersen(Aarhus University), Ole Bækgaard Nielsen(Aarhus University), Jesper Lausten(Aarhus University Hospital), Frank Vincenzo de Paoli(Aarhus University)
Cited by 19
Related Papers
The ClC-1 chloride channel inhibitor NMD670 improves skeletal muscle function in rat models and patients with myasthenia gravis
|Science Translational Medicine|2024|31
Extracellular magnesium and calcium reduce myotonia in ClC-1 inhibited rat muscle
|Neuromuscular Disorders|2013|25
The anti‐convulsants lacosamide, lamotrigine, and rufinamide reduce myotonia in isolated human and rat skeletal muscle
|Muscle & Nerve|2017|17
Divalent cation-responsive myotonia and muscle paralysis in skeletal muscle sodium channelopathy
|Neuromuscular Disorders|2015|7
Neuromuscular transmission deficits in patients with <scp>CMT</scp> and <scp>ClC</scp>‐1 inhibition in <scp>CMT</scp> animal models
|Annals of Clinical and Translational Neurology|2024|5