Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP.
Gergely L. Lukács(Hospital for Sick Children), Asmaa Mohamed(Hospital for Sick Children), Norbert Kartner(Hospital for Sick Children), X.B. Chang(Hospital for Sick Children), J.R. Riordan(Hospital for Sick Children), Sergio Grinstein(Hospital for Sick Children)
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